Linear scleroderma forehead treatment

Last UpdatedMarch 5, 2024

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GARD can help. Aug 25, 2022 · For severe or widespread morphea, treatment may include the use of ultraviolet light (phototherapy). Jan 18, 2022 · Linear scleroderma of the head and face is a rare connective tissue disorder characterized by linear depressed scarring in the frontoparietal area of the face. Systemic scleroderma Heart (systemic sclerosis) Linear morphea, the most common type of scleroderma in children, is characterized by lines of thickened skin, often on the arms, legs, head (usually on the forehead or scalp), or trunk. Autologous fat transplantation has been widely used, and fat appears to be an ideal material There are two generally recognized types of Localized scleroderma: morphea and linear. Scleroderma is a type of autoimmune disorder. Nov 14, 2023 · Causes. Treatment of linear scleroderma "en coup de sabre" with AlloDerm tissue matrix. Coping. These cases presented with linear dermal sclerosis on the forehead, oval subcutaneous and dermal depression in the cheek. May 12, 2009 · When linear scleroderma affects the head it is sometimes referred to as scleroderma en coup de sabre. This can affect the motion of joints and muscles as well as the growth of the affected area. If the diagnosis is scleroderma, treatment is most effective when started shortly after the disease has begun. 2008 Apr;138 (4):540-1. The color gradually evolved from reddish to purplish-grey and shiny within 3 months. 12 Sources. Here, we report a patient with linear scleroderma of the head and face with neurological symptoms such as spontaneous epilepsy and numbness of the right limb as well as the A: Your linear scleroderma involvement of the forehead and scalp is fairly classic, going down (or up) along the pathway of the 1st division of the trigeminal nerve. When it occurs as alopecia of the scalp, eyebrow, eyelashes, or forehead, it is termed linear scleroderma en coup de sabre (LSCS). otohns. 3. Linear Morphea is also known as Linear Scleroderma . Or your doctor may suggest hydroxychloroquine (Plaquenil) or Linear scleroderma causes lines of thickened or different colored skin to run down your arm, leg, and, rarely, on the forehead. The common plaque type usually causes no problems (apart from sometimes an unsightly appearance) and tends to fade in time. When it occurs on the scalp or forehead, it is termed "en coup de sabre". Medications can help you manage pain, but they may have other side effects that could be serious. Linear scleroderma is a progressive loss of subcutaneous fat with pigment changes in the skin. This line can appear on your arm, leg, or forehead. Conclusion: Autologous fat grafting provides a safe and easy approach for the treatment of linear scleroderma "en coups de sabre". You may have pain, stiffness or aches in your joints or muscles. Jun 24, 2013 · A. The en coup de sabre is a linear form of scleroderma that consists in furrowing of the skin of the forehead and front parietal region above the level of the eyebrow and often over the scalp Treatment of linear scleroderma "en coup de sabre" with AlloDerm tissue matrix. It can affect the trunk, arms, legs, face or neck, or multiple parts of the body. Systemic sclerosis and CRST syndrome. In the en coup de sabre subtype, many extracutaneous associations, mostly neurological, have been described. Treatment consisted of soft-tissue expansion and autologous bone grafting to the forehead, a composite graft for alar reconstruction, and a scalp graft for eyebrow reconstruction. There are some surgical therapeutic options for the treatment of residual atrophy. Scleroderma en coup de sabre is a form of linear scleroderma in which the line of skin thickening occurs on the forehead or elsewhere on the face. Scleroderma is an autoimmune condition that can lead to a tightening or hardening of the skin and, in some cases, internal organs. Nov 25, 2020 · Parry Romberg syndrome (PRS) is a disorder of unknown etiology which causes progressive hemifacial atrophy, affecting the skin, fat tissue, muscles, and bones. Joints: Stiffness, swelling and loss of mobility (how easily you can move your joint). With minimal manipulation of the aspirated fat, combined Scleroderma means “hard skin. Linear scleroderma is most common in young girls. Atrophy is when body tissue shrinks or wastes away. Figure 1. The cause of scleroderma is unknown. This type usually only affects the skin, but it can spread to your joints, muscles, or bones. Atrophic changes affect subcutaneous tissue and skin, with later involvement of the muscles Jan 27, 2012 · In scleroderma en coup de sabre (LScs) the atrophic lesion in frontoparietal area is the disease hallmark. There is controversy about whether en coup de sabre is truly a variant of linear Mar 19, 2021 · Based on the European and Japanese treatment guidelines for localized scleroderma, generalized, linear, and deep subtypes generally require systemic treatment. Scheme of Blaschko´s lines Linear scleroderma may affect the muscles and underlying bones, causing growth disturbance and ankylosis. A case of coup de sabre, a linear form of scleroderma, is presented. When it involves the lower face or produces hemifacial atrophy of deeper tissues, it is called progressive hemifacial atrophy (PHA), also known as the Parry-Romberg syndrome (PRS) (Fig. Porphyria cutanea tarda. Linear scleroderma tends to involve deeper layers of the skin as well as the surface layers, and sometimes restricts the movement of the joints that lie underneath. Oct 19, 2011 · Linear scleroderma is a line of thickened skin that occurs in areas such as the arms legs or forehead. Mixed connective tissue disease. 1 According to some reports, scleroderma (both local-ized and systemic) represents the third most com-mon rheumatologic condition in children after Oct 23, 2017 · 1. 037. By Lana Barhum. There are many forms, which Linear Morphea is one…which often Linear scleroderma is a form of localized scleroderma which frequently starts as a streak or line of hardened, waxy skin on an arm or leg or on the forehead. Morphea, also sometimes called “localized scleroderma,” is a rare autoimmune disorder that causes skin thickening, hardening, and color changes. The rash extends vertically from the hairline to the bridge of the nose. Besides the lesion in the face or scalp there are also Linear scleroderma can occur over the forehead, in a variant called en coup de sabre (Figure 43-11). Morphea is divided into subgroups that are based on clinical appearance and distribution. 1016/j. Failure to recognize and appropriately treat the affected skin and underlying deep connective tissue can lead to long-term morbidity. There are different types. Within the previous 2 years, the lesions had considerably progressed and resulted in a marked atrophy of subcutaneous tissue and bone structures on the left side of the face (figure C). If linear morphea symptoms affect your child’s face or scalp, the condition is known as “en coup de sabre” (French for “cut by a sword”). In dermatology, the medication typically is used in low doses. When scleroderma affects the heart or lungs, it can cause shortness of breath, decreased exercise tolerance and dizziness. It has been reported in both kids and adults with equal frequency. Linear scleroderma is the most common type of localized scleroderma in children; it is thought that 67% of cases of linear scleroderma are diagnosed before the age of 18. Because of the smaller dose, more severe side effects, such as extensive hair loss, which can be associated with methotrexate in other Apr 30, 2018 · Introduction. Mar 9, 2020 · Introduction. Plaque morphoea does not always need treatment because it usually improves on its own after a few years. Started early, treatments like phototherapy (light Linear scleroderma. It is a type of localized scleroderma in which the area of skin affected appears in a band. At that time, physical and occupational therapy can help you keep your ability to straighten and bend your joints and maintain your daily life. Learn about types, causes, risk factors, symptoms, diagnosis & treatment. Six patients had facial lesions. In some cases, this type of scleroderma affects deeper layers of the skin as well as underlying muscles and bone, potentially resulting in muscle weakness Information Center. Symptoms of en coup de sabre appear as an indented, vertical, colorless line of skin on their forehead. Linear scleroderma is more common in children. However, strong steroid creams or ointments or a non-steroid Feb 27, 2024 · Scleroderma is a long-lasting autoimmune disease that affects your skin, connective tissue, & internal organs. Many people who have scleroderma lead normal—or almost normal—lives. Linear scleroderma is a type of localized scleroderma that is most commonly diagnosed in children. There are two types of localized scleroderma – linear or morphea. The various clinical subtypes of LS require different approaches to evaluation and treatment. Mar 27, 2010 · Unfortunately the medical treatment was not successful and hence in June 2000 she underwent a number of surgical procedures including excision of the linear area of morphoea on the forehead Aug 7, 2023 · Morphea, also referred to as localized scleroderma, is a rare inflammatory disease of the skin and subcutaneous tissue. Disease Overview. It often is prescribed in pill form for morphea, and it can reduce symptoms effectively. May 1, 2020 · Background: Linear scleroderma, also known as "en coup de sabre," is a subtype of localized scleroderma that warrants aesthetic correction because it appears on the forehead region in children. The linear type can cause problems to underlying tissues such as muscles and bones. Linear scleroderma appears as lines or streaks of waxy, hardened skin, typically on the arms, legs, or forehead. You will find these marks on the stomach, back, chest, arms, and legs. It is a self-limiting condition which is thought to be autoimmune in origin. There was no history of preceding trauma Jun 17, 2015 · There are two types of localized scleroderma: Linear scleroderma will cause streaks of hardened skin on the forehead, legs, and arms. Sep 2, 2020 · September 2, 2020. The term scleroderma refers to hardened skin. 2a, b). In about 50% of patients the disease undergoes Linear scleroderma may leave its mark on the forehead. Symptoms. The case of a 54-year-old woman with a 3 and one-half year history of en coup de sabre is presented. Morphoea or localised scleroderma. Oct 13, 2023 · Linear morphea, also known as linear scleroderma, is a localized form of scleroderma characterized by the presence of lesions that follow a linear distribution pattern. Results: At 6 mo postoperatively, the patient had maintained a satisfactory correction of his left forehead and scalp regions with minimal resorption of fat. About 20% of patients can develop extracutaneous features including arthritis, uveitis, and seizures. doi: 10. Localized scleroderma is characterized by thickening of the skin from excessive collagen deposits. Apr 24, 2024 · When linear morphea occurs on the upper face, especially the paramedian forehead, it is often called en coup de sabre (ECDS) (Fig. It can rarely affect underlying muscle and bone and when severe can progress over years causing significant cosmetic, structural and functional disability. Within systemic scleroderma, there are 2 forms: Limited scleroderma progresses gradually. Linear scleroderma may coexist with progressive facial Jan 23, 2018 · Sometimes, linear morphea appears as a line on the forehead, which can cause problems with eyesight or lead to neurological problems. 1 The pansclerotic plaques are ivory in color with hyperpigmented to violaceous borders extending as a paramedian band on the The treatment for morphoea depends on the type (linear, plaque or generalised), the person’s age and whether it has spread deeper underneath the skin. 7 per 100,000, although this incidence has been increasing slightly since the 1960s. Morphea is seen more in adults, with increased incidence with advancing age, whereas linear scleroderma occurs more frequently in children and adolescents. It is characterized by abnormalities of the skin and subcutaneous tissues that often follow a dermatomal distribution and that are found on one side of the body. In this condition, the immune system mistakenly attacks and damages healthy body tissue. 2c–f). When linear scleroderma occurs on the anterior portion of the scalp and forehead, it may assume an ivory-like, depressed configuration Linear Morphea (Linear Scleroderma) —Linear morphea, which may or may not occur in a dermatomal distribution, manifests as a discrete linear induration that primarily affects the extremities. Lungs: Coughing and shortness of breath ( dyspnea ). This manifests as an overproduction of collagen, a protein that is a building block of connective Pain Medications. The underlying etiology of LM is still poorly understood, although some have suggested that morphea represents a mosaic form of systemic . Sep 29, 2023 · Systemic sclerosis can also cause symptoms in other organs and tissue, like your: Muscles: Numbness and swelling, especially in your hands and feet (your extremities). This affects the skin by causing it to be tight and shiny and can also affect internal organs, causing significant organ dysfunction. En coup de sabre (ECDS) is a rare subtype of linear scleroderma that is limited to the hemiface in a unilateral distribution. Treatment can help control the symptoms and limit damage. 1-888-205-2311. The linear form can involve deeper layers of the skin, which can cause constriction of the joints, and approximately 10-20% of people with Linear Scleroderma will develop joint pain. 2 ). Complications are deformities, joint contractures, and severe limb atrophy. 31 , 32 Children are more frequently affected than adults, but both sexes are affected equally. Linear scleroderma usually develops in childhood. WHAT CAUSES SCLERODERMA? Jul 29, 2011 · Linear scleroderma is a form of localized scleroderma that primarily affects the pediatric population. En coup de sabre variant of linear morphea (LM) is a rare sclerotic skin disorder characterized by disfiguring linear depression of the frontal or frontoparietal forehead. Dec 2, 2022 · For the head variant linear morphea cohort, patient charts were reviewed for demographics, age of morphea onset, disease subtype, morphea location, complications, treatment course, and response. According to the literature, involvement of the ‘on line Apr 27, 2016 · Background: Linear scleroderma, also known as "en coup de sabre," is a subtype of localized scleroderma that warrants aesthetic correction because it appears on the forehead region in children. The condition is further divided into two subgroups En coup de sabre is a type of linear scleroderma that presents on the frontal or frontoparietal scalp. 07. Sometimes it forms a long crease on the head or neck, referred to as en coup de sabre because it resembles a saber or sword wound. Although these problems can’t always be prevented, their effects may be minimized with proper treatment. Pain Medications. cosmetic deformities. 3–4 ), or can be limited to the forehead or scalp, where is it known as en coup de sabre ( Fig. It is often associated with the form of linear localized scleroderma (LS) on the scalp and forehead termed En Coup de Sabre (ECDS). When linear scleroderma occurs on the anterior portion of the scalp and forehead, it may assume an ivory-like, depressed configuration similar to the stroke of a sabre and called 'coup de sabre'. It can occur in more than one area. Apr 22, 2024 · More research is necessary to determine the long-term safety and effectiveness of immunosuppressive drugs in the treatment of Parry-Romberg syndrome. In growing children, both linear scleroderma and en coup de sabre can result in distortion of the growing limb or lack of symmetry of both sides of the face. Treatment. Patient with a linear scleroderma lesion (trilinear) on the forehead; B. 38 Although remissions are reported to occur in 3 to 5 years, ongoing clinical activity May 19, 2020 · Linear scleroderma “en coups de sabre” is a disease that causes scar-like lesions in the forehead and the scalp, and atrophy of the underlying structures. NSAIDs. The clinical presentation, laboratory findings, epidemiology, etiologic hypotheses, and treatment options are reviewed. In children the growth of the involved limb may be affected. Available toll-free Monday through Friday from 12 pm to 6 pm Eastern Time. Scleroderma can cause scarring in the lung tissues that may result in increasing shortness of breath over time. Jan 8, 2021 · We provide a simplified approach for the diagnosis of linear hyperpigmentation through two steps: 1 To determine whether hyperpigmentation follows Blaschko’s lines; 2 to determine the presence or absence of associated systemic manifestations in addition to other cutaneous findings ( Figures 1 and. Current attempts for cosmetic correction of atrophic lesions must be preceded by an evaluation of disease activity of LM, either by a sufficient clinical assessment or Dec 18, 2023 · Other Symptoms. The line can extend deep into the skin and affect the bones and muscles underneath it. Morphea scleroderma will cause oval patches of thickened skin that are purple around the edges and white in the middle. Apart from the typical inflammation and fibrosis of the skin, the linear subtype of morphea often affects underlying structures such as muscles and bones, which can lead to May 19, 2023 · Case Report: A 7-year-old boy presented with a linear, painless, non-itchy rash at the center of his forehead, which has been present for 6 months. While the pathophysiology of cutaneous linear scleroderma includes endothelial cell injury and up regulation of pro-fibrogenic pathways, the En coup de sabre is a type of linear scleroderma that presents on the frontal or frontoparietal scalp. He had underlying eczema, allergic May 16, 2019 · Linear scleroderma “en coup de sabre” (LSES) variant is a cephalic subtype of localized scleroderma that can be associated with extracutaneous stigmata, such as epilepsy, dementia syndromes, as well as focal central nervous system neurologic deficits. Sep 30, 2021 · Methotrexate is a drug that suppresses the immune system. This often affects deeper layers of skin, spreads over joints and may limit the movement of the joint. A type of localized scleroderma characterized by a long strip of indurated skin, which is typically found unilaterally on an arm or leg, and sometimes on the forehead or trunk. Mar 3, 2021 · With the other form, the main symptom is a line or band of skin that thickens and changes color. Scleroderma is an autoimmune condition in which the body produces too much collagen. It affects the skin on your fingers, hands, lower arms, legs Nov 10, 2021 · Linear scleroderma is a subtype of localised scleroderma. Where you have the hardening and tightening varies with the type of scleroderma you have. Although there is no cure for the condition, there are treatments available that can help relieve symptoms and improve your quality of life. At your age it would be fairly common that the disease process has burned itself out. Oct 20, 2022 · Linear scleroderma , also known as scleroderma en coup de saber, is a very focal form of scleroderma classically characterized by a linear band of atrophy involving the frontal or frontoparietal scalp and subjacent thinned calvaria associated with ipsilateral focal brain abnormalities. Otolaryngol Head Neck Surg. 10. Morphea encompasses a wide spectrum of clinical variants ranging from solitary skin lesions with minimal discomfort to severe subtypes like generalized or linear morphea. It often only affects the outer layer of skin but sometimes leads to more serious issues due to the involvement of deeper parts of the body. It is a chronic condition in which the immune system mistakenly activates in a way that damages your own body. Your treatment depends on the type of scleroderma you have, your symptoms, and which tissues and organs are affected. Oral medications. permanent eye damage in children. It most often occurs in the arms, legs, or forehead, and may occur in more than one area. 18,19 The recommended first-line therapy is methotrexate with or without systemic corticosteroids, and in case of treatment failure, mycophenolate mofetil is considered a second-line option. Aims Jul 21, 2021 · A 15-year-old girl presented to our outpatient clinic with a 10-year history of two band-like atrophic grooves located on the left part of the forehead (figure A, B). Jul 4, 2018 · Linear scleroderma of the face (en coup de sabre) is a disfiguring chronic skin disorder, often starting in childhood or adolescence. Lesions are usually limited and most commonly just one lesion is found. Talk with your rheumatologist about non-drug treatments to help manage pain too. There are various conditions that are affected by scleroderma or appear similar to it. Jul 1, 2021 · Linear morphea (LM) is a rare localized variant of scleroderma, and the term “en coup de sabre” (ECDS) refers to atrophic linear depression of the frontal or frontoparietal forehead extending to the scalp. Atrophic changes affect subcutaneous tissue and skin, with later involvement of the muscles and osteocartilaginous framework. Diagnosis. Dec 19, 2022 · Parry-Romberg syndrome affects the soft tissue and skin of a person’s face, causing it to atrophy. Joints, muscles, and even internal organs like the kidneys and lungs can harden and tighten. This disorder often affects the tissues beneath the skin, causing damage to bones, muscle or other organs. Also, special cosmetics and plastic surgery can help conceal scleroderma’s damage. Acrodermatitis chronica atrophicans. It is also most likely to be on just one side of the body. Morphea is a localized form of scleroderma and affects primarily just the skin. When linear scleroderma occurs on the anterior portion of the scalp and forehead, it may assume an ivory-like, depressed configuration similar to the stroke of a sabre and called ‘coup de sabre’. 2007. However, when too much collagen is made, the skin becomes stiff and hard. A buildup of a substance called collagen in the skin and other organs leads to the symptoms of the disease. Lipodermatosclerosis. 3-7 Milan and Bennett3 excised the involved skin and primarily closed the defect. Linear scleroderma of the head and face is a rare connective tissue disorder characterized by linear depressed scarring in the frontoparietal area of the face. Most often, scleroderma is seen on the arms, legs, and face but can occur anywhere. These cases pose a difficult differential diagnosis with Parry-Romberg syndrome. To date, various methods have been reported in the management of this deformity. a sabre or sword wound. joint pain. But this disease can affect more than the skin. Jan 18, 2022 · Abstract. If extensively covered, it may not allow the limb 3 days ago · Heart- and lung-related symptoms. Finding the right health care provider or getting the correct diagnosis may prove challenging. For severe or widespread morphea, your doctor may prescribe an immunosuppressive medication, such as oral methotrexate (Trexall), corticosteroid pills or both. BACKGROUND Facial linear scleroderma results in depressed atrophic scars. 1 According to some reports, scleroderma (both localized and systemic) represents Jul 22, 2014 · The scleroderma en coup de sabre is a type of linear scleroderma that may produce disfiguring scars. The involvement is unilateral in 95% of cases. It typically first appears in young children on one side of the body. skin and subcutaneous tissue. Pain is a common symptom for people living with scleroderma. Systemic scleroderma, also known as systemic sclerosis, may come on quickly or gradually and may also cause problems with your internal organs in addition to the skin. It involves the skin and can extend to the fascia, muscle, and bone. Skin and subcutaneous are the mainly affected tissues, but case reports of muscle, cartilage, and bone involvement are frequent. For some patients the use of immunosuppressive drugs may help with controlling seizures, especially when Parry-Romberg syndrome co-exists with linear scleroderma ‘en coup de sabre’. Localized scleroderma represents a group of connective tissue disorders that primarily affect the skin and subcutaneous tissue. Here, we report a patient with linear scleroderma of the head and face with neurological symptoms such as spontaneous epilepsy and numbness of the right limb as well as the presence of Discussion Due to the incidence in a young population and location on the forehead, linear scleroderma warrants aesthetic correction. 1 Among them are injectable fillers (hyaluronic acid, PMMA, calcium hydroxylapatite), transplanted or autologous fat grafting and resection of the lesion. The result is an acute facial asymmetry that can be distressing to affected young adults. Localized scleroderma or morphea, an autoimmune disorder, is the most common form of scleroderma in children. The lesional skin first exhibits contraction and stiffness that lead to characteristic fibrotic plaques with associated linear alopecia. Advantages of autologous fat grafting include the wide availability of donor tissue in most individuals, and the biocompatibility of the graft, with decreased risk of granulomatous or Aug 21, 2023 · This is a type of linear morphea, which is a type of localized scleroderma. Feb 13, 2008 · Linear scleroderma is a subtype of localised scleroderma. However morphea can occur in a generalized form as well as guttate, nodular, subcutaneous and linear forms. see a board certified dermatologist Helpful Treatment of Scleroderma. 2 Linear Scleroderma. Morphea is relatively uncommon and women are affected about three times as often as Localized scleroderma is a milder form of the disease. Bone graft causes morbidity at the donor site and is limited in forming a natural appearance of the margins [ 4 ]. 3–5 ). Morphea has an estimated annual population incidence of 2. A patient with linear scleroderma en coup de sabre was noted to have ipsilateral brain cavernomas by magnetic Linear scleroderma is a subtype of localised scleroderma. It affects bands or lines of tissue that can be deep and also affect the muscles; lesions are often present on the arms or legs. Mar 19, 2021 · Based on the European and Japanese treatment guidelines for localized scleroderma, generalized, linear, and deep subtypes generally require systemic treatment. Sep 26, 2017 · We reviewed six localized scleroderma cases that were initially treated with medication and then received follow-up surgery between April 2003 and February 2015. Nov 9, 2016 · Localised scleroderma causes one or more patches of hard skin. . Often no treatment is needed for the plaque type Nov 22, 2017 · Linear scleroderma and scleroderma don't necessarily go hand in hand but from your photo you may have linear scleroderma which may respond to filler not Botox. Feb 13, 2021 · Purpose of review Localized scleroderma (LS), also known as morphea, is a complex and poorly understood disorder in children. Scleroderma is characterized by the appearance of circumscribed or diffuse, hard, smooth, ivory-colored areas that are immobile and give the appearance of hidebound skin ( Andrews’ Diseases of the Skin ). ”. Linear scleroderma tends to involve deeper layers of the Aug 19, 2021 · A shiny, thickened streak of tough darker (or lighter) looking skin that may involve a leg or arm and may spread along a line to feet or hand, and sometimes to head, face, scalp, or forehead. Relevant clinical notes and laboratory/pathology/imaging findings were reviewed. 1. Linear scleroderma is one sub-type of localized scleroderma, most commonly occurring in childhood. 2 treatments . May 17, 2019 · One study involving 20 patients with linear scleroderma of the face showed 51–75% long-term correction of forehead lesions after an average of 4. It can limit movement, alter growth, and disfigure the Jul 7, 2017 · Morphea with deep lesions, lesions on your face or neck, or widespread lesions can lead to: restricted joint mobility. hair loss Mar 21, 2024 · Symptoms of scleroderma include thickened skin, skin color changes, stiff joints, muscle weakness, visible blood vessels, and more. Many people with this type of scleroderma have Treatment works best when started early. Instead of patches of thickened skin commonly seen in the morphea -type of localized scleroderma, patients with the linear type have thick streaks of skin usually affecting the limbs and torso. The disease most often affects people ages 30 to 50 years. 1 LSCS can cause significant functional disability and cosmetic Linear morphea of the forehead or en coup de sabre (ECDS) is an unusual variant of morphea. Various Linear is usually a waxy line or streak appearing on the arm, leg, or forehead and usually starts in childhood. Objective: To report dermal fat grafting as a novel and effective surgical treatment option in linear scleroderma. This type of morphea is more likely to affect school-aged Linear scleroderma is a type of localised scleroderma which is an autoimmune disease characterized by a line of thickened skin which can affect the bones and muscles underneath it. 1 Dec 1, 2008 · Autologous fat transplantation is an effective method for long-term correction of depressed atrophic scars left by linear scleroderma on the forehead but is less effective for corrections on the nose, infraorbital area, and chin. Several surgical treatments are available such as free tissue transfer and synthetic fillers. None of the linear scleroderma cases reported in the literature consisted of bony reconstruction. We present a review of the current Various treatment modalities for LScs have been introduced, such as bone graft for augmentation of the linear scleroderma at the forehead. Contact a GARD Information Specialist to receive the individualized support you may need. Collagen is a protein normally present in our skin that provides structural support. Parry-Romberg syndrome is a rare disorder Dec 23, 2015 · Linear scleroderma, also known as “en coup de sabre,” is a subtype of localized scleroderma that warrants aesthetic correction because it appears on the forehead region in children. It can occur as a single lesion, usually on an extremity, can be widespread (Fig. Apr 14, 2022 · Linear scleroderma is a localized scleroderma of unknown etiology characterized by band-like sclerotic lesions of the skin and underlying tissues. Your doctor may recommend medications, including: Anti-inflammatory medications to manage pain and reduce swelling. tu rm gt gv xz jg nk li ol ne